Cystic Fibrosis (CF)
In cystic fibrosis, mucus clogs the lungs and leads to recurrent, life-threatening infections and destruction of the lungs. The secretions may also block the pancreas, preventing enzymes from absorbing nutrients from food, and block the bile duct in the liver, causing permanent liver damage.
- Shortness of breath
- Persistent coughing with phlegm
- Poor weight gain
- Greasy stools
- Salty skin
- Cystic fibrosis is usually managed with medications. These medications include antibiotics and mucus thinners to prevent or clear up infection and improve lung function. Patients with CF also need to perform daily airway clearance exercises to dislodge mucus from the lungs.
- Patients with severe cystic fibrosis may require advanced medical therapy or a Lung Transplant. During a lung transplant, the diseased lungs are replaced with donor lungs.